Idiopathic Pulmonary Fibrosis
Idiopathic pulmonary fibrosis is a long-term condition in which the tissue around the air sacs in the lungs becomes scarred and thickened, making it harder for the lungs to work properly. The cause is unknown.
Key points
- Idiopathic pulmonary fibrosis often causes progressive shortness of breath and a dry cough that worsens over time.
- The listed medicine, pirfenidone, may help slow the decline in lung function.
Medicines listed for Idiopathic Pulmonary Fibrosis
The listed product Pirfenex is a tablet containing pirfenidone, an anti-fibrotic medicine. Pirfenidone belongs to a class of treatments that target the scarring process in the lungs, the central feature of pulmonary fibrosis.